What is the most likely diagnosis?
- 35 year-old whose pre-employment chest radiograph shows abnormal shadow
Frontal and Lateral Chest Radiograph
- Pneumomediastinum
- Sarcoid
- Neurofibroma
- Interrupted IVC with Azygos Continuation
- Mitral Stenosis
Additional Image - Enhanced axial CT images of chest and abdomen
Additional Images
Enhanced axial CT images of chest and abdomen
Answer:
4. Interrupted IVC with Azygos Continuation
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Interrupted IVC with Azygos Continuation
General Considerations
- Rare
- Frequently associated with other congenital anomalies
- Occurs in 0.6% of patients with congenital heart defects
- In usual form, the IVC is interrupted above level of renal veins
- There is absence of the hepatic segment of the IVC and the post-renal IVC continues as azygos and hemiazygos veins
- Embryologically, there is a failure to form right subcardinal–hepatic anastomosis resulting in atrophy of right subcardinal vein